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KMID : 0360220150560071141
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Journal of the Korean Ophthalmological Society
2015 Volume.56 No. 7 p.1141 ~ p.1148
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Three Cases of Outer Retinal Tubulation in Bietti’s Crystalline Dystrophy
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Kim Yong-Il
Kim In-Taek
Kim Jin-Seon
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Abstract
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Purpose: To report the prevalence and the characteristics of outer retinal tubulation (ORT) in Bietti’s crystalline dystrophy in 6 eyes of 3 patients.
Case summary: Three patients with Bietti’s crystalline dystrophy were examined using color fundus photography, fundus autofluorescence picture, spectral domain optical coherence tomography (SD-OCT), fluorescein angiography, electroretinogram and electrooculogram. ORT was detected in 3 of 3 (100%) Bietti’s crystalline dystrophy patients. SD-OCT B-scan revealed hyperreflective material inside the hyporeflective internal space with hyperreflective border. ORT was observed under the fovea or outside the fovea and on the outer nuclear layer in the retina. ORTs were no greater than 70 x 140 μm in size when measured using SD-OCT B-scan image.
Conclusions: ORT was observed frequently in patients with Bietti’s crystalline dystrophy. These findings can potentially predict the extensive photoreceptor abnormalities in retinal pigment epithelial atrophy.
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KEYWORD
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Bietti’s crystalline dystrophy, Outer retinal tubulation, Spectral domain optical coherence tomography
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